Malignant histiocytosis

Affects: Dogs

Overview

Malignant histiocytosis is a rare hereditary disease found in the Bernese Mountain Dog and humans, characterized by histiocytic infiltration of the lungs and lymph nodes. The liver, spleen, and central nervous system can also be affected. Histiocytes are a component of the immune system that proliferate abnormally in this disease. In addition to its importance in veterinary medicine, the condition is also important in human pathology.

Signs & Symptoms

Signs And Symptoms: The disease in the lungs is characterized by enlargement of the tracheobronchial lymph nodes and infiltration of the lungs, sometimes leading to lung lobe consolidation and pleural effusion. Signs and symptoms include cough, loss of appetite, weight loss, anemia, and difficulty breathing. Seizures and rear limb weakness can be seen. Invasion of the bone marrow can cause pancytopenia. Diagnosis requires a biopsy.

Treatment Approach

Treatment: Treatment with chemotherapy has been used with some success, particularly using lomustine, prednisone, doxorubicin, and cyclophosphamide. Because of the rapid progression of this aggressive disease, the prognosis is very poor.

Educational information only. This page is general guidance and is not a substitute for professional veterinary advice. Never give medicines or change treatment without consulting a veterinarian. If your pet is unwell, contact OC Pets or seek emergency care.
Sources (reused under open licences, with thanks): Wikipedia — “Malignant histiocytosis” (CC BY-SA 4.0) · Compiled by OC Pets Veterinary Clinic, updated 15-06-2026.